Wednesday, March 22, 2023
HomeDermatologyIncontinentia Pigmenti

Incontinentia Pigmenti


Incontinentia pigmenti is an X-linked dominant neurocutaneous syndrome with cutaneous, neurologic, ophthalmologic, and dental manifestations. Garrod reported the first probable case of incontinentia pigmenti in 1906 and described it as a peculiar pigmentation of the skin in an infant. Subsequently, Bloch and Sulzberger further defined the condition in 1926 and 1928, respectively, as a clinical syndrome with a constellation of unique features that includes typical cutaneous manifestations.

- Advertisment -

Most Popular